G40.834 Dravet syndrome, intractable, without status epilepticus

Instructional Notes:

G40.834
Description: Dravet syndrome, intractable, without status epilepticus
Inclusion Term:
- Dravet syndrome NOS
↓
G40.83
Description: Dravet syndrome
Inclusion Term:
- Polymorphic epilepsy in infancy (PMEI)
- Severe myoclonic epilepsy in infancy (SMEI)
↓
G40.8
Description: Other epilepsy and recurrent seizures
Inclusion Term:
- Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized
- Landau-Kleffner syndrome
↓
G40
Description: Epilepsy and recurrent seizures
Exclude1:
- conversion disorder with seizures (F44.5)
- convulsions NOS (R56.9)
- post traumatic seizures (R56.1)
- seizure (convulsive) NOS (R56.9)
- seizure of newborn (P90)
Exclude2:
- hippocampal sclerosis (G93.81)
- mesial temporal sclerosis (G93.81)
- temporal sclerosis (G93.81)
- Todd's paralysis (G83.84)
Notes:
- the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
↓
G40-G47
Description: Episodic and paroxysmal disorders (G40-G47)
↓
G00-G99
Description: Diseases of the nervous system
Exclude2:
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)